CHDI
2020
Authors
Title
Journal
- Messer A, | Butler DC |Optimizing intracellular antibodies (intrabodies/nanobodies) to treat neurodegenerative disordersNeurobiol Dis104619134():20200203PMID:31669671Julayanont P, | McFarland NR, | Heilman KM |Mild cognitive impairment and dementia in motor manifest Huntington's disease: Classification and prevalenceJ Neurol Sci116523408():20200115PMID:31678902Cariulo C, | Verani M, | Martufi P, | Ingenito R, | Finotto M, | Deguire SM, | Lavery DJ, | Toledo-Sherman L, | Lee R, | Doherty EM, | Vogt TF, | Dominguez C, | Lashuel HA, | Petricca L, | Caricasole A |Ultrasensitive quantitative measurement of huntingtin phosphorylation at residue S13Biochem Biophys Res Commun549-554521(3):20200115PMID:31677786Bertoglio D, | Verhaeghe J, | Korat Š, | Miranda A, | Cybulska K, | Wyffels L, | Stroobants S, | Mrzljak L, | Dominguez C, | Skinbjerg M, | Liu L, | Munoz-Sanjuan I, | Staelens S |Elevated type 1 metabotropic glutamate receptor availability in a mouse model of Huntington's disease: a longitudinal PET studyMol Neurobiol():20200110PMID:31912442Pflanz CP, | Charquero-Ballester M, | Majid DSA, | Winkler AM, | Vallée E, | Aron AR, | Jenkinson M, | Douaud G |One-year changes in brain microstructure differentiate preclinical Huntington's disease stagesNeuroimage Clin10209925():20200106PMID:31865023
2019
AuthorsTitleJournal- Aviolat H, | Pinto RM, | Godschall E, | Murtha R, | Richey HE, | Sapp E, | Vodicka P, | Wheeler VC, | Kegel-Gleason KB, | DiFiglia M |Assessing average somatic CAG repeat instability at the protein levelSci Rep191529(1):20191216PMID:31844074Bertoglio D, | Verhaeghe J, | Korat Š, | Miranda A, | Wyffels L, | Stroobants S, | Mrzljak L, | Dominguez C, | Liu L, | Skinbjerg M, | Munoz-Sanjuan I, | Staelens S |In vitro and In vivo assessment of suitable reference region and kinetic modelling for the mGluR1 radioligand [(11)C] ITDM in miceMol Imaging Biol():20191202PMID:31792838Smarr B, | Cutler T, | Loh DH, | Kudo T, | Kuljis D, | Kriegsfeld L, | Ghiani CA, | Colwell CS |Circadian dysfunction in the Q175 model of Huntington's disease: Network analysisJ Neurosci Res1606-162397(12):20191202PMID:31359503DOI: 10.1002/jnr.24505Papadopoulou AS, | Gomez-Paredes C, | Mason MA, | Taxy BA, | Howland D, | Bates GP |Extensive expression analysis of Htt transcripts in brain regions from the zQ175 HD mouse model using a QuantiGene multiplex assaySci Rep161379(1):20191106PMID:31695145Marottoli FM, | Priego M, | Flores-Barrera E, | Pisharody R, | Zaldua S, | Fan KD, | Ekkurthi GK, | Brady ST, | Morfini GA, | Tseng KY, | Tai LM |EGF treatment improves motor behavior and cortical GABAergic function in the R6/2 mouse model of Huntington's diseaseMol Neurobiol7708-771856(11):20191105PMID:31104296PMCID: 6815691Gregory S, | Odish OFF, | Mayer I, | Mills J, | Johnson EB, | Scahill RI, | Rothwell J, | Rees G, | Long JD, | Tabrizi SJ, | Roos RAC, | Orth M |Multimodal characterization of the visual network in Huntington's disease gene carriersClin Neurophysiol2053-2059130(11):20191101PMID:31541982Ciosi M, | Maxwell A, | Cumming SA, | Hensman Moss DJ, | Alshammari AM, | Flower MD, | Durr A, | Leavitt BR, | Roos RAC, | TRACK-HD team, | Enroll-HD team | Holmans P, | Jones L, | Langbehn DR, | Kwak S, | Tabrizi SJ, | Monckton DG |A genetic association study of glutamine-encoding DNA sequence structures, somatic CAG expansion, and DNA repair gene variants, with Huntington disease clinical outcomesEBioMedicine568-58048():20191030PMID:31607598Diaz-Castro B, | Gangwani MR, | Yu X, | Coppola G, | Khakh BS |Astrocyte molecular signatures in Huntington's diseaseSci Transl Medeaaw854611(514):20191016PMID:31619545Haremaki T, | Metzger JJ, | Rito T, | Ozair MZ, | Etoc F, | Brivanlou AH |Self-organizing neuruloids model developmental aspects of Huntington's disease in the ectodermal compartmentNat Biotechnol1198-120837(10):20191011PMID:31501559Kim KH, | Abu Elneel K, | Shin JW, | Keum JW, | Seong D, | Kwak S, | Lee R, | Gusella JF, | MacDonald ME, | Seong IS, | Lee JM |Full sequence of mutant huntingtin 3'-untranslated region and modulation of its gene regulatory activity by endogenous microRNAJ Hum Genet995-100464(10):20191001PMID:31296921Khakh BS |Astrocyte-neuron interactions in the striatum: insights on identity, form, and functionTrends Neurosci617-63042(9):20190904PMID:31351745van der Plas E, | Langbehn DR, | Conrad AL, | Koscik TR, | Tereshchenko A, | Epping EA, | Magnotta VA, | Nopoulos PC |Abnormal brain development in child and adolescent carriers of mutant huntingtinNeurologye1021-e103093(10):20190903PMID:31371571Kubera KM, | Schmitgen MM, | Hirjak D, | Wolf RC, | Orth M |Cortical neurodevelopment in pre-manifest Huntington's diseaseNeuroimage Clin10191323():20190902PMID:31491822PMCID: 6627026Wanker EE, | Ast A, | Schindler F, | Trepte P, | Schnoegl S |The pathobiology of perturbed mutant huntingtin protein-protein interactions in Huntington's diseaseJ Neurochem():20190816PMID:31418858DOI: 10.1111/jnc.14853Swainson LA, | Ahn H, | Pajanirassa P, | Khetarpal V, | Deleage C, | Estes JD, | Hunt PW, | Munoz-Sanjuan I, | McCune JM |Kynurenine 3-Monooxygenase inhibition during acute simian immunodeficiency virus infection lowers PD-1 expression and improves post-combination antiretroviral therapy CD4(+) T cell counts and body weightJ Immunol899-910203(4):20190815PMID:31285277PMCID: 6684450Langbehn DR, | Stout JC, | Gregory S, | Mills JA, | Durr A, | Leavitt BR, | Roos RAC, | Long JD, | Owen G, | Johnson HJ, | Borowsky B, | Craufurd D, | Reilmann R, | Landwehrmeyer GB, | Scahill RI, | Tabrizi SJ, | TRACK-HD and Track-On HD Groups |Association of CAG repeats with long-term progression in Huntington diseaseJAMA Neurol():20190812PMID:31403680Federspiel JD, | Greco TM, | Lum KK, | Cristea IM |Hdac4 interactions in Huntington's disease viewed through the prism of MultiomicsMol Cell ProteomicsS92-S11318(8):20190809PMID:31040226GeM-HD Consortium, | Lee JM, | Correia K, | Loupe J, | Kim KH, | Barker D, | Hong EP, | Chao MJ, | Long JD, | Lucente D, | Vonsattel JPG, | Pinto RM, | Abu Elneel K, | Ramos EM, | Mysore JS, | Gillis T, | Wheeler VC, | MacDonald ME, | Gusella JF, | McAllister B, | Massey T, | Medway C, | Stone TC, | Hall L, | Jones L, | Holmans P, | Kwak S, | Ehrhardt AG, | Sampaio C, | Ciosi M, | Maxwell A, | Chatzi A, | Monckton DG, | Orth M, | Landwehrmeyer GB, | Paulsen JS, | Dorsey ER, | Shoulson I, | Myers RH |CAG repeat not polyglutamine length determines timing of Huntington's disease onsetCell887-900178(4):20190808PMID:31398342PMCID: 6700281Huhtala T, | Poutiainen P, | Rytkönen J, | Lehtimäki K, | Parkkari T, | Kasanen I, | Airaksinen AJ, | Koivula T, | Sweeney P, | Kontkanen O, | Wityak J, | Dominiquez C, | Park LC |Improved synthesis of [(18)F] fallypride and characterization of a Huntington's disease mouse model, zQ175DN KI, using longitudinal PET imaging of D2/D3 receptorsEJNMMI Radiopharm Chem204(1):20190805PMID:31659519Alterman JF, | Godinho BMDC, | Hassler MR, | Ferguson CM, | Echeverria D, | Sapp E, | Haraszti RA, | Coles AH, | Conroy F, | Miller R, | Roux L, | Yan P, | Knox EG, | Turanov AA, | King RM, | Gernoux G, | Mueller C, | Gray-Edwards HL, | Moser RP, | Bishop NC, | Jaber SM, | Gounis MJ, | Sena-Esteves M, | Pai AA, | DiFiglia M, | Aronin N, | Khvorova A |A divalent siRNA chemical scaffold for potent and sustained modulation of gene expression throughout the central nervous systemNat Biotechnol884-89437(8):20190802PMID:31375812Kacher R, | Lamazière A, | Heck N, | Kappes V, | Mounier C, | Despres G, | Dembitskaya Y, | Perrin E, | Christaller W, | Sasidharan Nair S, | Messent V, | Cartier N, | Vanhoutte P, | Venance L, | Saudou F, | Néri C, | Caboche J, | Betuing S |CYP46A1 gene therapy deciphers the role of brain cholesterol metabolism in Huntington's diseaseBrain2432-2450142(8):20190801PMID:31286142DOI: 10.1093/brain/awz174Bertoglio D, | Verhaeghe J, | Miranda A, | Kertesz I, | Cybulska K, | Korat Š, | Wyffels L, | Stroobants S, | Mrzljak L, | Dominguez C, | Liu L, | Skinbjerg M, | Munoz-Sanjuan I, | Staelens S |Validation and noninvasive kinetic modeling of [(11) C] UCB-J PET imaging in miceJ Cereb Blood Flow Metab():20190731PMID:31307287Flower M, | Lomeikaite V, | Ciosi M, | Cumming S, | Morales F, | Lo K, | Hensman Moss D, | Jones L, | Holmans P, | TRACK-HD Investigators, | OPTIMISTIC Consortium, | Monckton DG, | Tabrizi SJ |MSH3 modifies somatic instability and disease severity in Huntington's and myotonic dystrophy type 1Brain1876–1886142(7):20190715PMID:31216018DOI: 10.1093/brain/awz115PMCID: 6598626Wilkes FA, | Abaryan Z, | Ching CRK, | Gutman BA, | Madsen SK, | Walterfang M, | Velakoulis D, | Stout JC, | Chua P, | Egan GF, | Thompson PM, | Looi JCL, | Georgiou-Karistianis N |Striatal morphology and neurocognitive dysfunction in Huntington disease: the IMAGE-HD studyPsychiatry Res Neuroimaging1-8291():20190712PMID:31330407Franich NR, | Hickey MA, | Zhu C, | Osborne GF, | Ali N, | Chu T, | Bove NH, | Lemesre V, | Lerner RP, | Zeitlin SO, | Howland D, | Neueder A, | Landles C, | Bates GP, | Chesselet MF |Phenotype onset in Huntington's disease knock-in mice is correlated with the incomplete splicing of the mutant huntingtin geneJ Neurosci Res1590-160597(12):20190708PMID:31282030DOI: 10.1002/jnr.24493Zeitler B, | Froelich S, | Marlen K, | Shivak DA, | Yu Q, | Li D, | Pearl JR, | Miller JC, | Zhang L, | Paschon DE, | Hinkley SJ, | Ankoudinova I, | Lam S, | Guschin D, | Kopan L, | Cherone JM, | Nguyen HB, | Qiao G, | Ataei Y, | Mendel MC, | Amora R, | Surosky R, | Laganiere J, | Vu BJ, | Narayanan A, | Sedaghat Y, | Tillack K, | Thiede C, | Gärtner A, | Kwak S, | Bard J, | Mrzljak L, | Park L, | Heikkinen T, | Lehtimäki KK, | Svedberg MM, | Häggkvist J, | Tari L, | Tóth M, | Varrone A, | Halldin C, | Kudwa AE, | Ramboz S, | Day M, | Kondapalli J, | Surmeier DJ, | Urnov FD, | Gregory PD, | Rebar EJ, | Muñoz-Sanjuán I, | Zhang HS |Allele-selective transcriptional repression of mutant HTT for the treatment of Huntington's diseaseNat Med1131-114225(7):20190701PMID:31263285Bigan E, | Sasidharan Nair S, | Lejeune FX, | Fragnaud H, | Parmentier F, | Mégret L, | Verny M, | Aaronson J, | Rosinski J, | Neri C |Genetic cooperativity in multi-layer networks implicates cell survival and senescence in the striatum of Huntington's disease mice synchronous to symptomsBioinformatics():20190624PMID:31228193Poudel GR, | Harding IH, | Egan GF, | Georgiou-Karistianis N |Network spread determines severity of degeneration and disconnection in Huntington's diseaseHum Brain Mapp1-10():20190612PMID:31187915DOI: 10.1002/hbm.24695Huguet G, | Temel Y, | Kádár E, | Pol S, | Casaca-Carreira J, | Segura-Torres P, | Jahanshahi A |Altered expression of dopaminergic cell fate regulating genes prior to manifestation of symptoms in a transgenic rat model of Huntington's diseaseBrain Res101-1081712():20190601PMID:30711400Ochaba J, | Fote G, | Kachemov M, | Thein S, | Yeung SY, | Lau AL, | Hernandez S, | Lim RG, | Casale M, | Neel MJ, | Monuki ES, | Reidling J, | Housman DE, | Thompson LM, | Steffan JS |IKKβ slows Huntington's disease progression in R6/1 miceProc Natl Acad Sci USA10952-10961116(22):20190528PMID:31088970Octeau JC, | Gangwani MR, | Allam SL, | Tran D, | Huang S, | Hoang-Trong TM, | Golshani P, | Rumbell TH, | Kozloski JR, | Khakh BS |Transient, consequential increases in extracellular potassium ions accompany Channelrhodopsin2 excitationCell Rep2249-2261.e727(8):20190521PMID:31116972PMCID: 6582980Dvorzhak A, | Helassa N, | Török K, | Schmitz D, | Grantyna R |Single synapse indicators of impaired glutamate clearance derived from fast iGlu u imaging of cortical afferents in the striatum of normal and Huntington (Q175) miceJ Neurosci3970-398239(20):20190515PMID:30819797Svedberg MM, | Varnäs K, | Varrone A, | Mitsios N, | Mulder J, | Gulyás B, | Beaumont V, | Munoz-Sanjuan I, | Zaleska MM, | Schmidt CJ, | Halldin C, | Mrzljak L |In vitro phosphodiesterase 10A (PDE10A) binding in whole hemisphere human brain using the PET radioligand [(18)F] MNI-659Brain Res140-1451711():20190515PMID:30664847Holley SM, | Galvan L, | Kamdjou T, | Dong A, | Levine MS, | Cepeda C |Major contribution of somatostatin-expressing interneurons and cannabinoid receptors to increased GABA synaptic activity in the striatum of Huntington's disease miceFront Synaptic Neurosci11(14):20190514PMID:31139071PMCID: 6527892Sharma M, | Subramaniam S |Rhes travels from cell to cell and transports Huntington disease protein via TNT-like protrusionJ Cell Biolpii: jcb.201807068():20190510PMID:31076452Pido-Lopez J, | Tanudjojo B, | Farag S, | Bondulich MK, | Andre R, | Tabrizi SJ, | Bates GP |Inhibition of tumour necrosis factor alpha in the R6/2 mouse model of Huntington's disease by etanercept treatmentSci Rep72029(1):20190510PMID:31076648PMCID: 6510744Shahn Z, | Li Y, | Sun Z, | Mohan A, | Sampaio C, | Hu J |G-Computation and hierarchical models for estimating multiple causal effects from observational disease registries with irregular visitsAMIA Jt Summits Transl Sci Proc789-7982019():20190506PMID:31259036PMCID: 6568089Di Marco A, | Gonzalez Paz O, | Fini I, | Vignone D, | Cellucci A, | Battista MR, | Auciello G, | Orsatti L, | Zini M, | Monteagudo E, | Khetarpal V, | Rose M, | Dominguez C, | Herbst T, | Toledo-Sherman L, | Summa V, | Muñoz-Sanjuán I |Application of an in vitro blood-brain barrier model in the selection of experimental drug candidates for the treatment of Huntington's diseaseMol Pharm2069-208216(5):20190506PMID:30916978Shoulson I, | Eberly S, | Oakes D, | Kayson E, | Young AB | PHAROS Investigators |Phenotype-genotype discrepancies in the prospective Huntington at-risk observational studyAnn Clin Transl Neurol1046-10526(6):20190503PMID:31211168DOI: 10.1002/acn3.781PMCID: 6562068Vizcarra JA, | Sánchez-Ferro Á, | Maetzler W, | Marsili L, | Zavala L, | Lang AE, | Martinez-Martin P, | Mestre TA, | Reilmann R, | Hausdorff JM, | Dorsey ER, | Paul SS, | Dexheimer JW, | Wissel BD, | Fuller RLM, | Bonato P, | Tan AH, | Bloem BR, | Kopil C, | Daeschler M, | Bataille L, | Kleiner G, | Cedarbaum JM, | Klucken J, | Merola A, | Goetz CG, | Stebbins GT, | Espay AJ | MDS Technology Task Force and | MDS Rating Scales Program Electronic Development Ad-Hoc Committee |The Parkinson's disease e-diary: Developing a clinical and research tool for the digital ageMov Disord676-68134(5):20190501PMID:30901492DOI: 10.1002/mds.27673Kojer K, | Hering T, | Bazenet C, | Weiss A, | Herrmann F, | Taanman JW, | Orth M |Huntingtin aggregates and mitochondrial pathology in skeletal muscle but not heart of late-stage R6/2 miceJ Huntingtons Dis145–1598(2):20190430PMID:30814364DOI: 10.3233/JHD-180324Harding RJ, | Loppnau P, | Ackloo S, | Lemak A, | Hutchinson A, | Hunt B, | Holehouse AS, | Ho JC, | Fan L, | Toledo-Sherman L, | Seitova A, | Arrowsmith CH |Design and characterization of mutant and wildtype huntingtin proteins produced from a toolkit of scalable eukaryotic expression systemsJ Biol Chem6986-7001294(17):20190426PMID:30842263Carrillo-Reid L, | Day M, | Xie Z, | Melendez AE, | Kondapalli J, | Plotkin JL, | Wokosin DL, | Chen Y, | Kress GJ, | Kaplitt M, | Ilijic E, | Guzman JN, | Chan SS, | Surmeier DJ |Mutant huntingtin enhances activation of dendritic Kv4 K(+) channels in striatal spiny projection neuronsElifee408188():20190424PMID:31017573DOI: 10.7554/eLife.40818Espinoza FA, | Liu J, | Ciarochi J, | Turner JA, | Vergara VM, | Caprihan A, | Misiura M, | Johnson HJ, | Long JD, | Bockholt JH, | Paulsen JS, | Calhoun VD |Dynamic functional network connectivity in Huntington's disease and its associations with motor and cognitive measuresHum Brain Mapp1955-196840(6):20190415PMID:30618191DOI: 10.1002/hbm.24504Todorov DI, | Capps RA, | Barnett WH, | Latash EM, | Kim T, | Hamade KC, | Markin SN, | Rybak IA, | Molkov YI |The interplay between cerebellum and basal ganglia in motor adaptation: A modeling studyPLoS Onee021492614(4):20190412PMID:30978216PMCID: 6461234Tang X, | Ross CA, | Johnson H, | Paulsen JS, | Younes L, | Albin RL, | Ratnanather JT, | Miller MI |Regional subcortical shape analysis in premanifest Huntington's diseaseHum Brain Mapp1419-143340(5):20190401PMID:30376191DOI: 10.1002/hbm.24456Toledo-Sherman L, | Breccia P, | Cachope R, | Bate JR, | Angulo-Herrera I, | Wishart G, | Matthews KL, | Martin SL, | Cox HC, | McAllister G, | Penrose SD, | Vater H, | Esmieu W, | Van de Poël A, | Van de Bospoort R, | Strijbosch A, | Lamers M, | Leonard P, | Jarvis RE, | Blackaby W, | Barnes K, | Eznarriaga M, | Dowler S, | Smith GD, | Fischer DF, | Lazari O, | Yates D, | Rose M, | Jang SW, | Muñoz-Sanjuan I, | Dominguez C |Optimization of potent and selective ataxia telangiectasia-mutated inhibitors suitable for a proof-of-concept study in Huntington's disease modelsJ Med Chem2988-300862(6):20190328PMID:30840447Reindl W, Baldo B, Schulz J, Janack I, Lindner I, Kleinschmidt M, | Sedaghat Y, | Thiede C, | Tillack K, | Schmidt C, | Cardaun I, | Schwagarus T, | Herrmann F, | Hotze M, | Osborne GF, | Herrmann S, | Weiss A, | Zerbinatti C, | Bates GP, | Bard J, | Munoz-Sanjuan I, | Macdonald D |Meso scale discovery-based assays for the detection of aggregated huntingtinPLoS Onee021352114(3):20190326PMID:30913220Murthy V, | Tebaldi T, | Yoshida T, | Erdin S, | Calzonetti T, | Vijayvargia R, | Tripathi T, | Kerschbamer E, | Seong IS, | Quattrone A, | Talkowski ME, | Gusella JF, | Georgopoulos K, | MacDonald ME, | Biagioli M |Hypomorphic mutation of the mouse Huntington's disease gene orthologuePLoS Genete100776515(3):20190321PMID:30897080Zlebnik NE, | Gildish I, | Sesia T, | Fitoussi A, | Cole EA, | Carson BP, | Cachope R, | Cheer JF |Motivational impairment is accompanied by corticoaccumbal dysfunction in the BACHD-Tg5 rat model of Huntington's diseaseCereb Cortex():20190228PMID:30753343Merienne N, | Meunier C, | Schneider A, | Seguin J, | Nair SS, | Rocher AB, | Le Gras S, | Keime C, | Faull R, | Pellerin L, | Chatton JY, | Neri C, | Merienne K, | Déglon N |Cell-type-specific gene expression profiling in adult mouse brain reveals normal and disease-state signaturesCell Rep2477-249326(9):20190226PMID:30811995Castaldo I, | De Rosa M, | Romano A, | Zuchegna C, | Squitieri F, | Mechelli R, | Peluso S, | Borrelli C, | Del Mondo A, | Salvatore E, | Vescovi LA, | Migliore S, | De Michele G, | Ristori G, | Romano S, | Avvedimento EV, | Porcellini A |DNA damage signatures in peripheral blood cells as biomarkers in prodromal huntington diseaseAnn Neurol296-30185(2):20190221PMID:30549309DOI: 10.1002/ana.25393Kang R, | Wang L, | Sanders SS, | Zuo K, | Hayden MR, | Raymond LA |Altered regulation of striatal neuronal N-Methyl-D-Aspartate receptor trafficking by palmitoylation in Huntington disease mouse modelFront Synaptic Neurosci11(3):20190221PMID:30846936PMCID: 6393405Goold R, | Flower M, | Moss DH, | Medway C, | Wood-Kaczmar A, | Andre R, | Farshim P, | Bates GP, | Holmans P, | Jones L, | Tabrizi SJ |FAN1 modifies Huntington's disease progression by stabilizing the expanded HTT CAG repeatHum Mol Genet650-66128(4):20190215PMID:30358836DOI: 10.1093/hmg/ddy375PMCID: 6360275Gatto RG, | Ye AQ, | Colon-Perez L, | Mareci TH, | Lysakowski A, | Price SD, | Brady ST, | Karaman M, | Morfini G, | Magin RL |Detection of axonal degeneration in a mouse model of Huntington's disease: comparison between diffusion tensor imaging and anomalous diffusion metricsMAGMA():20190215PMID:30771034Tousley A, | Iuliano M, | Weisman E, | Sapp E, | Richardson H, | Vodicka P, | Alexander J, | Aronin N, | DiFiglia M, | Kegel-Gleason KB |Huntingtin associates with the actin cytoskeleton and α-actinin isoforms to influence stimulus dependent morphology changesPLoS Onee021233714(2):20190215PMID:30768638Smatlikova P, | Juhas S, | Juhasova J, | Suchy T, | Hubalek Kalbacova M, | Ellederova Z, | Motlik J, | Klima J |Adipogenic differentiation of bone marrow-derived mesenchymal stem cells in pig transgenic model expressing human mutant huntingtinJ Huntingtons Dis33-518(1):20190213PMID:30584151DOI: 10.3233/JHD-180303Rieke L, | Fels M, | Schubert R, | Habbel B, | Matheis T, | Schuldenzucker V, | Kemper N, | Reilmann R |Activity behaviour of minipigs transgenic for the Huntington geneJ Huntingtons Dis23-318(1):20190213PMID:30689591DOI: 10.3233/JHD-180325Perez-Rosello T, | Gelman S, | Tombaugh G, | Cachope R, | Beaumont V, | Surmeier DJ |Enhanced striatopallidal gamma-aminobutyric acid (GABA)(A) receptor transmission in mouse models of huntington's diseaseMov Disord684-69634(5):20190206PMID:30726572DOI: 10.1002/mds.27622Ciarochi JA, | Johnson HJ, | Calhoun VD, | Liu J, | Espinoza FA, | Bockholt HJ, | Misiura M, | Caprihan A, | Plis S, | Paulsen JS, | Turner JA, | PREDICT-HD Investigators and Coordinators of the Huntington Study Group |Concurrent cross-sectional and longitudinal analyses of multivariate white matter profiles and clinical functioning in pre-diagnosis Huntington diseaseJ Huntingtons Dis199-2198(2):20190205PMID:30932891DOI: 10.3233/JHD-180332Padovan-Neto FE, | Jurkowski L, | Murray C, | Stutzmann GE, | Kwan M, | Ghavami A, | Beaumont V, | Park LC, | West AR |Age- and sex-related changes in cortical and striatal nitric oxide synthase in the Q175 mouse model of Huntington's diseaseNitric Oxide40-5083():20190201PMID:30528913Paulsen JS, | Lourens S, | Kieburtz K, | Zhang Y |Sample enrichment for clinical trials to show delay of onset in Huntington diseaseMov Disord274-28034(2):20190201PMID:30644132DOI: 10.1002/mds.27595Holley SM, | Galvan L, | Kamdjou T, | Cepeda C, | Levine MS |Striatal GABAergic interneuron dysfunction in the Q175 mouse model of Huntington's diseaseEur J Neurosci79-9349(1):20190130PMID:30472747DOI: 10.1111/ejn.14283Rodrigues FB, | Byrne LM, | De Vita E, | Johnson EB, | Hobbs NZ, | Thornton JS, | Scahill RI, | Wild EJ |Cerebrospinal fluid flow dynamics in Huntington's disease evaluated by phase contrast MRIEur J Neurosci1-8():20190128PMID:30687961DOI: 10.1111/ejn.14356Lu M, | Banetta L, | Young LJ, | Smith EJ, | Bates GP, | Zaccone A, | Kaminski Schierle GS, | Tunnacliffe A, | Kaminski CF |Live-cell super-resolution microscopy reveals a primary role for diffusion in polyglutamine-driven aggresome assemblyJ Biol 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2018
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